Early myoclonic encephalopathy.
نویسندگان
چکیده
Early myoclonic encephalopathy (EME) is a rare malignant epileptic syndrome. The erratic myoclonus with or without focal motor seizures, onset before 3 months of age, and persistent suppression-burst pattern in electroencephalograph (EEG) are accepted as the diagnostic criteria for EME. We report an 11 month old infant with EME which was secondary to non-ketotic hyperglycinemia.
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عنوان ژورنال:
- Indian pediatrics
دوره 46 9 شماره
صفحات -
تاریخ انتشار 2009